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Successful Desensitization Protocol to Ivacaftor and a Compound of Elexacaftor/Tezacaftor/Ivacaftor in a Delayed Hypersensitivity Reaction Confirmed by Lymphocyte Transformation Test

Mir-Ihara P1, De Las Vecillas L1,2,3, Heredia R1, Fiandor A1,2,3, González-Muñoz M2,4, Zamarrón E2,5, Prados C2,5, Cabañas R1,2,3,6

1Allergy Department. Hospital Universitario La Paz, Madrid, Spain
2Hospital La Paz Institute for Health Research (IdiPAZ), Madrid, Spain
3PIELenRed Consortium
4Immunology Department. Hospital Universitario La Paz, Madrid, Spain
5Pulmonary Department. Hospital Universitario La Paz, Madrid, Spain
6Center for Biomedical Research Network on Rare Diseases (CIBERER U754), Madrid, Spain

J Investig Allergol Clin Immunol 2024; Vol. 34(3)
doi: 10.18176/jiaci.0961

Key words: Cystic fibrosis, Cystic fibrosis transmembrane conductance modulators, Desensitization, Delayed hypersensitivity, Lymphocyte transformation test